Isolated unilateral absence of adult pulmonary artery

Case Reports

. 2022 Nov 27;10(11):e6652.

doi: 10.1002/ccr3.6652.

eCollection 2022 Nov.

Affiliations

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Case Reports

Koichiro Yamamoto et al.

Clin Case Rep.

2022.

Abstract

Isolated unilateral absence of pulmonary artery (UAPA) is a rare congenital malformation. We describe a 26-year-old woman with isolated UAPA who presented with hemoptysis. Since massive hemoptysis may mandate selective embolization of collaterals or surgical treatment, early diagnosis of UAPA is pivotal.

Keywords:

collateral artery; congenital heart disease; hemoptysis.

Conflict of interest statement

The authors declare no conflicts of interest.

Figures

FIGURE 1

(A) Ipsilateral cardiac and mediastinal displacement and the absence of pulmonary artery shadow are shown by chest X‐ray. (B, C) Contrast‐enhanced computed tomography (CT) (B) and three‐dimensional reconstructed CT (C) show the absence of the left pulmonary artery and the left pulmonary vascular bundles. The asterisk indicates the right pulmonary artery (B). Right‐sided aortic arch is also shown. (D) CT aortography showed tortuous collateral vessels from an inferior phrenic artery and an internal thoracic artery.

References

1. Kruzliak P, Syamasundar RP, Novak M, Pechanova O, Kovacova G. Unilateral absence of pulmonary artery: pathophysiology, symptoms, diagnosis and current treatment. Arch Cardiovasc Dis. 2013;106:448‐454.
  
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1. Wang P, Yuan L, Shi J, Xu Z. Isolated unilateral absence of pulmonary artery in adulthood: a clinical analysis of 65 cases from a case series and systematic review. J Thorac Dis. 2017;9:4988‐4996.
  
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