Successful biventricular repair in a 14-year-old patient of asplenia with congenital heart disease syndrome

Case Reports

doi: 10.1111/jocs.17171.

Online ahead of print.


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Case Reports

Yujie Weng et al.

J Card Surg.



Heterotaxy syndrome is a rare disease, and asplenia with congenital heart disease syndrome, also known as Ivemark syndrome, is a special form of heterotaxy syndrome. These patients usually have severe cardiovascular malformations and a poor prognosis. Their surgical outcomes are rarely satisfactory. We report the case of a 14-year-old patient who underwent successful corrective surgery treatment.


Ivemark syndrome; heterotaxy syndrome.



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