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A 16-Year Natural History of a Congenital Pseudoaneurysm of the Mitral-Aortic Intervalvular Fibrosa


Case Reports

. 2022 Jun 15;4(12):706-709.


doi: 10.1016/j.jaccas.2022.05.002.

Affiliations

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Case Reports

James A Bishara et al.


JACC Case Rep.


.

Abstract

Pseudoaneurysm of the mitral aortic intervalvular fibrosa is a rare condition most often reported as sequela of endocarditis and surgical trauma, with congenital cases being very uncommon. This case describes a congenital pseudoaneurysm of the mitral aortic intervalvular fibrosa and stable 16-year natural history. (Level of Difficulty: Intermediate.).


Keywords:

AOV, aortic valve; MV, mitral valve; PMAIF, pseudoaneurysm of the mitral-aortic intervalvular fibrosa; bicuspid aortic valve; congenital heart disease; echocardiography; mitral valve.

Conflict of interest statement

The authors have reported that they have no relationships relevant to the contents of this paper to disclose.

Figures



Graphical abstract


Figure 1


Figure 1

Comparison of Long Axis Comparison of parasternal long-axis view demonstrating the aortic valve and mitral valve with the pseudoaneurysm (arrow) seen within the left atrium (LA) posterior to the anterior leaflet of the mitral valve. (A) Two months of age. (B) Sixteen years of age. LV = left ventricle.


Figure 2


Figure 2

Comparison of Apical 4-Chamber Comparison of an apical 4-chamber view demonstrating the pseudoaneurysm (arrow) seen within the LA. (A) Two months of age. (B) Sixteen years of age. Ao = aorta; other abbreviations as in Figure 1.


Figure 3


Figure 3

Comparison of Short Axis Comparison of parasternal short-axis view showing the spherical pseudoaneurysm (arrow) toward the left and irregular tissue adjacent that extends along the underside of the atrial reflection of the aortic root. (A) Two months of age. (B) Sixteen years of age. RA = right atrium; RV = right ventricle.

References

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      PMC



      PubMed



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